Objective: Presentation of a case of isolated renal hydatid cyst with novel findings and unusual surgical scenario. Clinical Presentation and Intervention: A 54-year-old female patient presented with left loin pain and a palpable left renal mass. Imaging described a welldemarcated left renal cystic lesion with a two-layer wall. Radical nephrectomy was done due to the possibility of malignancy. On retrograde revision, the two-layer wall represented the detached germinative membrane of a hydatid cyst that was confirmed by histopathology. Conclusion: Isolated renal hydatid cyst could be misinterpreted as a renal tumor. It should be considered in the differential diagnosis of renal cystic lesions.